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Acetyl-CoA
acetyltransferase,
mitochondrial
Hydroxymethylglutaryl-
CoA synthase,
cytoplasmic
3-Hydroxy-3-
methylglutaryl-
coenzyme A
reductase
Mevalonate
kinase
Phosphomevalonate
kinase
Diphosphomevalonate
decarboxylase
Isopentenyl-
diphosphate
Delta-isomerase
1
Farnesyl
pyrophosphate
synthase
Farnesyl
pyrophosphate
synthase
Squalene
synthase
Squalene
monooxygenase
Lanosterol
synthase
Acetyl-CoA
Acetoacetyl-CoA
CoA
H
2
O
3-Hydroxy-3-methylglutaryl-CoA
CoA
H
+
Mevalonic acid
CoA
NADP
H
+
NADPH
ATP
Mevalonic acid-5P
ADP
H
+
ATP
ADP
(R)-Mevalonic
acid-5-pyrophosphate
ATP
ADP
CO
2
Isopentenyl pyrophosphate
P
i
Dimethylallylpyrophosphate
Isopentenyl pyrophosphate
Geranyl-PP
PP
i
Isopentenyl pyrophosphate
Farnesyl pyrophosphate
PP
i
H
+
NADPH
PP
i
NADP
Squalene
O
2
FMNH2
(S)-2,3-Epoxysqualene
H
+
H
2
O
Flavin Mononucleotide
Lanosterol
Magnesium
Magnesium
Magnesium
Magnesium
FAD
Glycolysis
Endoplasmic Reticulum
Membrane
Mitochondria
Endoplasmic Reticulum
Peroxisome
Cytoplasm
Nucleus
Endoplasmic Reticulum
ACAT1
HMGCS1
HMGCR
MVK
PMVK
MVD
IDI1
FDPS
FDPS
FDFT1
SQLE
LSS
Acetyl-CoA
Acetoacetyl-CoA
Coenzyme A
Water
3-Hydroxy-3-
methylglutaryl-
CoA
Coenzyme A
Hydrogen Ion
Mevalonic acid
Coenzyme A
NADP
Hydrogen Ion
NADPH
Adenosine
triphosphate
Mevalonic
acid-5P
Adenosine
diphosphate
Hydrogen Ion
Adenosine
triphosphate
Adenosine
diphosphate
(R)-Mevalonic
acid-5-
pyrophosphate
Adenosine
triphosphate
Adenosine
diphosphate
Carbon dioxide
Isopentenyl
pyrophosphate
Phosphate
Dimethylallylpyrophosphate
Isopentenyl
pyrophosphate
Geranyl-PP
Pyrophosphate
Isopentenyl
pyrophosphate
Farnesyl
pyrophosphate
Pyrophosphate
Hydrogen Ion
NADPH
Pyrophosphate
NADP
Squalene
Oxygen
FMNH2
(S)-2,3-
Epoxysqualene
Hydrogen Ion
Water
Flavin
Mononucleotide
Lanosterol
Glycolysis