Carnitine O-
palmitoyltransferase
1, liver isoform
Long-chain
fatty acid
transport
protein 1
Mitochondrial
carnitine/acylcarnitine
carrier protein
Organic
cation/carnitine
transporter 2
Long-chain-
fatty-acid--CoA
ligase 1
Carnitine O-
palmitoyltransferase
1, liver isoform
Acetyl-CoA
carboxylase 1
Malonyl-CoA
decarboxylase,
mitochondrial
Carnitine O-
palmitoyltransferase
2, mitochondrial
Carnitine O-
acetyltransferase
Acetyl-CoA
5-Hydroxydec-4-
enoyl-CoA
5-hydroxydec-4-
enoic acid
5-hydroxydec-4-
enoic acid
5-Hydroxydec-4-
enoylcarnitine
5-Hydroxydec-4-
enoylcarnitine
L-Carnitine
ATP
CoA
5-Hydroxydec-4-
enoyl-CoA
AMP
PPi
L-Carnitine
CoA
Acetyl-CoA
Malonyl-CoA
CO2
CoA
L-Carnitine
L-Carnitine
L-Acetylcarnitine
CoA
Magnesium
Biotin
Manganese
TCA Cycle
Mitochondrial
Beta-Oxidation
of Long Chain
Saturated Fatty
Acids
Mitochondrial Outer Membrane
Mitochondrial Inner Membrane
Extracellular Space
Cytosol
Intermembrane Space
Mitochondrial Matrix