Carnitine O-
palmitoyltransferase
1, liver
isoform
Long-chain
fatty acid
transport
protein 1
Mitochondrial
carnitine/acylcarnitine
carrier protein
Organic
cation/carnitine
transporter 2
Long-chain-
fatty-acid--
CoA ligase 1
Carnitine O-
palmitoyltransferase
1, liver
isoform
Acetyl-CoA
carboxylase 1
Malonyl-CoA
decarboxylase,
mitochondrial
Carnitine O-
palmitoyltransferase
2,
mitochondrial
Carnitine O-
acetyltransferase
Acetyl-CoA
(4Z,7Z,10Z,13Z,16Z)-
19,20-
dihydroxydocosa-
4,7,10,13,16-
pentaenoyl- CoA
(4Z,7Z,10Z,13Z,16Z)-
19,20-
dihydroxydocosa-
4,7,10,13,16-
pentaenoic acid
(4Z,7Z,10Z,13Z,16Z)-
19,20-
dihydroxydocosa-
4,7,10,13,16-
pentaenoic acid
(4Z,7Z,10Z,13Z,16Z)-
19,20-
dihydroxydocosa-
4,7,10,13,16-
pentaenoylcarnitine
(4Z,7Z,10Z,13Z,16Z)-
19,20-
dihydroxydocosa-
4,7,10,13,16-
pentaenoylcarnitine
L-Carnitine
ATP
CoA
(4Z,7Z,10Z,13Z,16Z)-
19,20-
dihydroxydocosa-
4,7,10,13,16-
pentaenoyl- CoA
AMP
PPi
L-Carnitine
CoA
Acetyl-CoA
Malonyl-CoA
CO2
CoA
L-Carnitine
L-Carnitine
L-
Acetylcarnitine
CoA
Magnesium
Biotin
Manganese
TCA Cycle
Mitochondrial
Beta-Oxidation
of Long Chain
Saturated Fatty
Acids
Mitochondrial Outer Membrane
Mitochondrial Inner Membrane
Extracellular Space
Cytosol
Intermembrane Space
Mitochondrial Matrix