Quantitative metabolomics services for biomarker discovery and validation.
Specializing in ready to use metabolomics kits.
Your source for quantitative metabolomics technologies and bioinformatics.
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Low affinity cationic amino acid transporter 2 Mitochondrial ornithine transporter 2 Unknown Solute carrier family 13 member 3 Alpha- aminoadipic semialdehyde synthase, mitochondrial Alpha- aminoadipic semialdehyde synthase, mitochondrial Alpha- aminoadipic semialdehyde dehydrogenase Kynurenine/alpha- aminoadipate aminotransferase, mitochondrial Enoyl-CoA hydratase, mitochondrial Hydroxyacyl- coenzyme A dehydrogenase, mitochondrial Acetyl-CoA acetyltransferase, mitochondrial Peroxisomal sarcosine oxidase Glutaryl-CoA dehydrogenase, mitochondrial Oxoglutarate dehydrogenase complex Medium-chain specific acyl-CoA dehydrogenase, mitochondrial Methylglutaconyl- CoA hydratase, mitochondrial Succinate-- hydroxymethylglutarate CoA-transferase Acetyl-CoA L-Lysine L-Lysine L-Lysine Allysine Allysine 3-Hydroxyglutaric acid 3-Hydroxyglutaric acid NADPH Oxoglutaric acid Saccharopine NADP H2O H2O NAD L-Glutamic acid NADH NAD H2O Aminoadipic acid NADH Oxoglutaric acid Oxoadipic acid L-Glutamic acid 3-Hydroxybutyryl-CoA Crotonoyl-CoA H2O NAD Acetoacetyl-CoA NADH CoA L-Pipecolic acid O2 (S)-2,3,4,5- Tetrahydropiperidine-2- carboxylate H2O2 Glutaryl-CoA CO2 CoA H2O H+ Glutaconyl-CoA H2O 3-Hydroxy-3-methylglutaryl-CoA Succinate Succinyl-CoA Pyridoxal 5'-phosphate Thiamine pyrophosphate Lipoamide FAD FAD Oxidized flavoprotein Reduced flavoprotein Solute carrier family 13 member 3 Citric Acid Cycle Biotin Metabolism FAD FAD Inner Mitochondria Membrane Outer Mitochondria Membrane Mitochondrial Intermembrane Space Peroxisome Mitochondria Extracellular Space Intracellular Space Liver Extracellular Space Mitochondrial matrix Liver Hepatic Cell Symptoms include encephalopathy, grimacing, dystonia, metabolic acidosis, and hygroma.