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Search for 'valine AND leucine' in 'all pathways' in 'Homo sapiens' returned 52 results

SMP0000200

Pw000069 View Pathway
Disease

Methylmalonic Aciduria

  • Matched Compounds: L-Leucine … L-Valine
  • Matched Compound Synonyms: (2s)-alpha-leucine … (s)-(+)-leucine … (s)-leucineLeucine … (2s)-a-leucine
  • SMP0000523

    Pw000499 View Pathway
    Disease

    Isobutyryl-CoA Dehydrogenase Deficiency

  • Matched Description: error of metabolism (IEM) of valine metabolism. It is an autosomal recessive disorder that is caused … the metabolism of branched-chain amino acids, specifically valine. This enzyme is responsible for … the third step in the breakdown of valine and converts isobutyryl-CoA into methylacrylyl-CoA. Defects … in the IBD enzyme function lead to elevated levels of valine in blood and other biofluids … energy. Treatment may include the use of L-carnitine supplements, frequent meals, and a low-valine diet.
  • Matched Compounds: L-Leucine … L-Valine
  • Matched Compound Synonyms: (2s)-alpha-leucine … (s)-(+)-leucine … (s)-leucineLeucine … (2s)-a-leucine
  • SMP0000199

    Pw000064 View Pathway
    Disease

    Maple Syrup Urine Disease

  • Matched Description: for a protein which is vital in the breakdown of amino acids, specifically the amino acids leucine … , isoleucine and valine. This disorder is characterized by a large accumulation of these amino acids
  • Matched Compounds: L-Leucine … L-Valine
  • Matched Compound Synonyms: (2s)-alpha-leucine … (s)-(+)-leucine … (s)-leucineLeucine … (2s)-a-leucine
  • SMP0000291

    Pw000359 View Pathway
    Drug Action

    Doxycycline Action Pathway

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine
  • SMP0000293

    Pw000361 View Pathway
    Drug Action

    Oxytetracycline Action Pathway

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine
  • SMP0000256

    Pw000354 View Pathway
    Drug Action

    Neomycin Action Pathway

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine
  • SMP0000249

    Pw000347 View Pathway
    Drug Action

    Clindamycin Action Pathway

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine
  • SMP0000731

    Pw000708 View Pathway
    Drug Action

    Josamycin Action Pathway

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine
  • SMP0000711

    Pw000688 View Pathway
    Drug Action

    Tobramycin Action Pathway

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine
  • SMP0000713

    Pw000690 View Pathway
    Drug Action

    Arbekacin Action Pathway

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine