Cystinosin
Aspartate
aminotransferase,
cytoplasmic
3-
mercaptopyruvate
sulfurtransferase
L-lactate
dehydrogenase
A-like 6A
Cysteine
dioxygenase type
1
Cystathionine
gamma-lyase
Aspartate
aminotransferase,
cytoplasmic
Glutamate--
cysteine ligase
Cysteine--tRNA
ligase,
cytoplasmic
L-Glutamic acid
γ-
Glutamylcysteine
3-Sulfinoalanine
Pyruvic acid
L-Cysteine
L-Cysteine
Oxoglutaric acid
3-Sulfinylpyruvic
acid
L-Glutamic acid
H2O
Sulfite
3-Mercaptopyruvic
acid
Cyanide
Thiocyanate
3-Mercaptolactic
acid
NAD
NADH
O2
H2O
Hydrogen sulfide
NH3
Oxoglutaric acid
L-Glutamic acid
ATP
ADP
Pi
ATP
AMP
PPi
Fe2+
Pyridoxal
5'-phosphate
tRNA(Cys)
L-
Cysteinyl-
tRNA(Cys)
Glutamate
Metabolism
Glutamate
Metabolism
Taurine and
Hypotaurine
Metabolism
Sulfate/Sulfite
Metabolism
Pyruvate
Metabolism
Methionine
Metabolism
Glycine and
Serine
Metabolism
Pantothenate
and CoA
Biosynthesis
Pyridoxal
5'-phosphate
Pyridoxal
5'-phosphate
Zinc (II) ion
Lysosome
Cytosol
Extracellular Space