Neutral amino
acid
transporter
B(0)
Neutral amino
acid
transporter A
Alanine
aminotransferase
1
Glutaminase liver
isoform,
mitochondrial
Glutamate
dehydrogenase 1,
mitochondrial
Carbamoyl-
phosphate
synthase
[ammonia],
mitochondrial
Aspartate
aminotransferase,
mitochondrial
Ornithine
carbamoyltransferase,
mitochondrial
Arginase-1
Argininosuccinate
lyase
Argininosuccinate
synthase
L-Glutamine
L-Alanine
Oxoglutaric acid
L-Glutamic acid
Oxalacetic acid
NH3
L-Aspartic acid
Fumaric acid
L-Arginine
Ornithine
L-Glutamine
L-Alanine
Ornithine
Citrulline
Citrulline
L-Aspartic acid
L-Glutamic acid
L-Glutamic acid
Pyruvic acid
H2O
H2O
NAD
Oxoglutaric acid
NADH
ATP
CO2
H2O
ADP
Pi
Carbamoyl
phosphate
Pi
H2O
Urea
Argininosuccinic
acid
ATP
AMP
PPi
Ammonia
Recycling
Pyrimidine
Metabolism
Glutamate
Metabolism
Alanine
Metabolism
Glucose-Alanine
Cycle
Selenoamino
Acid Metabolism
Malate-
Aspartate
Shuttle
Glutamate
Metabolism
Alanine
Metabolism
Glucose-Alanine
Cycle
Gluconeogenesis
Histidine
Metabolism
Porphyrin
Metabolism
Glucose-Alanine
Cycle
Porphyrin
Metabolism
Alanine
Metabolism
Ammonia
Recycling
Glutamate
Metabolism
Glucose-Alanine
Cycle
Ammonia
Recycling
Purine
Metabolism
Glucose-Alanine
Cycle
Aspartate
Metabolism
Citric Acid
Cycle
Arginine and
Proline
Metabolism
D-Arginine and
D-Ornithine
Metabolism
D-Arginine and
D-Ornithine
Metabolism
Mitochondrial
ornithine
transporter 1
Mitochondrial
ornithine
transporter 1
Calcium-binding
mitochondrial
carrier protein
Aralar1
Pyridoxal
5'-phosphate
Pyridoxal
5'-phosphate
Manganese
Calcium
Cytosol
Mitochondria
Mitochondrial Matrix
Urea Cycle
Extracellular Space
Intracellular Space