Quantitative metabolomics services for biomarker discovery and validation.
Specializing in ready to use metabolomics kits.
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Voltage- dependent anion-selective channel protein 1 Mitochondrial pyruvate carrier 1 Solute carrier family 22 member 8 Pyruvate dehydrogenase complex Citrate synthase, mitochondrial Isocitrate dehydrogenase [NAD] subunit alpha, mitochondrial Isocitrate dehydrogenase [NAD] subunit beta, mitochondrial Isocitrate dehydrogenase [NAD] subunit gamma, mitochondrial Oxoglutarate dehydrogenase complex Succinyl-CoA ligase Fumarate hydratase, mitochondrial Pyruvate carboxylase, mitochondrial Succinate dehydrogenase Aconitate hydratase, mitochondrial Aconitate hydratase, mitochondrial Malate dehydrogenase, mitochondrial Pyruvic acid Pyruvic acid Pyruvic acid Oxoglutaric acid Oxoglutaric acid CoA NAD Acetyl-CoA CO2 NADH H2O Oxalacetic acid Citric acid CoA Isocitric acid NAD CO2 NADH H+ NAD CoA Succinyl-CoA NADH H+ CO2 Pi GDP Succinic acid CoA GTP L-Malic acid Fumaric acid H2O ATP HCO3- ADP Pi Q FAD QH2 FADH2 cis-Aconitic acid H2O H2O NAD NADH H+ Thiamine pyrophosphate Lipoamide FAD Magnesium Thiamine pyrophosphate Lipoamide FAD Biotin Manganese 4Fe-4S 4Fe-4S Solute carrier family 22 member 8 Cytosol Mitochondrial matrix Mitochondrion Inner mitochondrial membrane Outer mitochondrial membrane TCA Cycle Intermembrane space Symptoms of the disorder include opisthotonus, ataxia, developmental delay, and seizures.